If a variant has more than one submission, it may be counted in more than one significance column. If this is the
case, the total number of variants will be less than the sum of the other cells.
Gene and significance breakdown #
Total genes and gene combinations: 98
| Gene or gene combination |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
total |
|
RYR1
|
16
|
21
|
2229
|
911
|
49
|
3226
|
|
RYR2
|
1
|
0 |
1575
|
831
|
78
|
2485
|
|
BRCA2
|
246
|
17
|
1282
|
611
|
50
|
2206
|
|
APC
|
36
|
10
|
1293
|
504
|
14
|
1857
|
|
DSP
|
29
|
47
|
1089
|
403
|
21
|
1589
|
|
TSC2
|
4
|
2
|
846
|
538
|
104
|
1494
|
|
FBN1
|
12
|
24
|
906
|
495
|
36
|
1473
|
|
MSH6
|
90
|
16
|
853
|
385
|
7
|
1351
|
|
MYBPC3
|
69
|
21
|
723
|
352
|
18
|
1183
|
|
SCN5A
|
27
|
26
|
697
|
400
|
25
|
1175
|
|
CACNA1S
|
1
|
1
|
805
|
319
|
37
|
1163
|
|
ATP7B
|
114
|
59
|
607
|
297
|
14
|
1091
|
|
BRCA1
|
116
|
11
|
474
|
307
|
32
|
940
|
|
MYH7
|
13
|
24
|
540
|
334
|
24
|
935
|
|
MYH11
|
0 |
1
|
496
|
302
|
33
|
832
|
|
COL3A1
|
8
|
16
|
515
|
280
|
12
|
831
|
|
MSH2
|
18
|
8
|
580
|
207
|
8
|
821
|
|
LDLR
|
88
|
70
|
376
|
220
|
5
|
759
|
|
KCNH2
|
16
|
10
|
390
|
259
|
21
|
696
|
|
RET
|
12
|
7
|
440
|
213
|
4
|
676
|
|
DSG2
|
2
|
1
|
451
|
188
|
19
|
661
|
|
PKP2
|
30
|
8
|
408
|
201
|
14
|
661
|
|
PCSK9
|
2
|
1
|
412
|
198
|
20
|
633
|
|
PMS2
|
51
|
15
|
358
|
179
|
10
|
613
|
|
TSC1
|
3
|
1
|
369
|
169
|
44
|
586
|
|
DSC2
|
0 |
0 |
406
|
153
|
8
|
567
|
|
MLH1
|
27
|
8
|
358
|
158
|
8
|
559
|
|
MYH11, NDE1
|
0 |
0 |
317
|
181
|
23
|
521
|
|
RB1
|
0 |
0 |
312
|
163
|
33
|
508
|
|
MUTYH
|
54
|
30
|
288
|
127
|
7
|
506
|
|
KCNQ1
|
40
|
25
|
230
|
150
|
14
|
459
|
|
LMNA
|
5
|
6
|
244
|
119
|
6
|
380
|
|
STK11
|
1
|
0 |
191
|
175
|
2
|
369
|
|
TMEM43
|
1
|
0 |
253
|
88
|
10
|
352
|
|
PRKAG2
|
0 |
1
|
200
|
124
|
9
|
334
|
|
BMPR1A
|
1
|
1
|
210
|
103
|
5
|
320
|
|
TGFBR2
|
1
|
2
|
187
|
105
|
6
|
301
|
|
MEN1
|
7
|
2
|
172
|
101
|
2
|
284
|
|
NF2
|
0 |
3
|
175
|
80
|
5
|
263
|
|
TP53
|
14
|
10
|
146
|
90
|
2
|
262
|
|
TNNT2
|
6
|
6
|
146
|
74
|
3
|
235
|
|
SMAD4
|
2
|
0 |
113
|
108
|
0 |
223
|
|
SMAD3
|
1
|
5
|
111
|
96
|
5
|
218
|
|
TGFBR1
|
1
|
1
|
128
|
73
|
3
|
206
|
|
BRCA1, LOC126862571
|
28
|
0 |
93
|
55
|
6
|
182
|
|
TNNI3
|
2
|
6
|
108
|
58
|
4
|
178
|
|
MYL3
|
0 |
2
|
114
|
41
|
10
|
167
|
|
PTEN
|
10
|
1
|
90
|
66
|
0 |
167
|
|
SDHB
|
18
|
6
|
106
|
30
|
1
|
161
|
|
LOC126861897, MHRT, MYH7
|
1
|
1
|
106
|
43
|
3
|
154
|
|
ACTA2
|
2
|
0 |
74
|
73
|
3
|
152
|
|
LOC110121269, SCN5A
|
1
|
2
|
100
|
47
|
2
|
152
|
|
LOC126806068, RYR2
|
0 |
0 |
98
|
50
|
4
|
152
|
|
TPM1
|
1
|
3
|
67
|
72
|
5
|
148
|
|
LOC107982234, WT1
|
0 |
0 |
97
|
48
|
1
|
146
|
|
ACTC1, GJD2-DT
|
0 |
0 |
46
|
85
|
2
|
133
|
|
WT1
|
0 |
2
|
76
|
52
|
3
|
133
|
|
VHL
|
0 |
1
|
91
|
34
|
0 |
126
|
|
MYL2
|
0 |
0 |
80
|
36
|
3
|
119
|
|
MHRT, MYH7
|
0 |
1
|
75
|
31
|
1
|
108
|
|
GLA, RPL36A-HNRNPH2
|
10
|
5
|
72
|
20
|
0 |
107
|
|
SDHC
|
4
|
8
|
61
|
27
|
0 |
100
|
|
OTC
|
3
|
1
|
56
|
35
|
1
|
96
|
|
SDHAF2
|
5
|
6
|
70
|
14
|
1
|
96
|
|
SDHD
|
6
|
1
|
64
|
21
|
0 |
92
|
|
LOC126861898, MYH7
|
3
|
8
|
42
|
29
|
4
|
86
|
|
LOC107303340, VHL
|
2
|
1
|
47
|
33
|
0 |
83
|
|
LOC126806067, RYR2
|
0 |
0 |
52
|
16
|
5
|
73
|
|
LOC126862902, RYR1
|
0 |
0 |
44
|
16
|
1
|
61
|
|
LOC130062899, STK11
|
0 |
0 |
24
|
18
|
1
|
43
|
|
LOC114827850, MYL2
|
1
|
1
|
18
|
11
|
1
|
32
|
|
FBN1, LOC113939944
|
0 |
0 |
20
|
8
|
1
|
29
|
|
KCNQ1, KCNQ1OT1
|
1
|
1
|
15
|
10
|
1
|
28
|
|
FBN1, LOC126862124
|
0 |
0 |
18
|
6
|
1
|
25
|
|
LOC129391106, RYR1
|
0 |
0 |
15
|
9
|
0 |
24
|
|
DSG2, LOC130062340
|
0 |
0 |
17
|
5
|
1
|
23
|
|
DSC2, DSCAS
|
0 |
0 |
14
|
7
|
1
|
22
|
|
LMNA, LOC126805877
|
2
|
0 |
15
|
4
|
1
|
22
|
|
LOC126861897, MYH7
|
0 |
0 |
19
|
3
|
0 |
22
|
|
COL3A1, LOC126806446
|
0 |
1
|
9
|
10
|
1
|
21
|
|
LDLR, MIR6886
|
2
|
2
|
4
|
7
|
0 |
15
|
|
LOC126861339, SDHD
|
0 |
0 |
7
|
8
|
0 |
15
|
|
MUTYH, TOE1
|
0 |
1
|
11
|
3
|
0 |
15
|
|
LOC130057352, SMAD3
|
1
|
1
|
6
|
5
|
1
|
14
|
|
FBN1, LOC130057019
|
1
|
0 |
8
|
2
|
2
|
13
|
|
LMNA, LOC129931597
|
0 |
1
|
9
|
3
|
0 |
13
|
|
LOC106736614, RET
|
0 |
0 |
9
|
4
|
0 |
13
|
|
LOC129933707, MSH6
|
1
|
0 |
8
|
4
|
0 |
13
|
|
LOC129929542, SDHB
|
1
|
0 |
6
|
2
|
0 |
9
|
|
LOC130064357, RYR1
|
0 |
0 |
7
|
0 |
0 |
7
|
|
PKD1, TSC2
|
0 |
0 |
0 |
3
|
4
|
7
|
|
APC, LOC129994371
|
0 |
0 |
4
|
0 |
0 |
4
|
|
APOB
|
2
|
0 |
1
|
0 |
0 |
3
|
|
LOC130058210, TSC2
|
0 |
0 |
3
|
0 |
0 |
3
|
|
COL3A1, MIR3606
|
0 |
0 |
0 |
2
|
0 |
2
|
|
LOC130003710, RET
|
0 |
0 |
0 |
2
|
0 |
2
|
|
GLA, HNRNPH2, RPL36A-HNRNPH2
|
1
|
0 |
0 |
0 |
0 |
1
|
|
LOC129929541, SDHB
|
0 |
0 |
1
|
0 |
0 |
1
|
Condition and significance breakdown #
| Condition |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
total |
|
Lynch syndrome
|
187
|
47
|
2157
|
933
|
33
|
3357
|
|
Malignant hyperthermia, susceptibility to, 1
|
16
|
21
|
2295
|
936
|
50
|
3318
|
|
Catecholaminergic polymorphic ventricular tachycardia
|
1
|
0 |
1725
|
897
|
87
|
2710
|
|
Hypertrophic cardiomyopathy
|
92
|
67
|
1366
|
779
|
52
|
2356
|
|
Tuberous sclerosis syndrome
|
7
|
3
|
1218
|
710
|
152
|
2090
|
|
Classic or attenuated familial adenomatous polyposis
|
36
|
10
|
1297
|
504
|
14
|
1861
|
|
Arrhythmogenic cardiomyopathy with wooly hair and keratoderma
|
29
|
47
|
1089
|
403
|
21
|
1589
|
|
Marfan syndrome
|
13
|
24
|
952
|
511
|
40
|
1540
|
|
Familial thoracic aortic aneurysm and aortic dissection
|
2
|
1
|
887
|
556
|
59
|
1505
|
|
Cardiomyopathy
|
0 |
0 |
912
|
514
|
35
|
1461
|
|
Breast-ovarian cancer, familial, susceptibility to, 2
|
133
|
9
|
824
|
442
|
30
|
1438
|
|
Arrhythmogenic right ventricular cardiomyopathy
|
32
|
9
|
876
|
394
|
34
|
1345
|
|
Cardiac arrhythmia
|
0 |
0 |
789
|
447
|
27
|
1263
|
|
Long QT syndrome
|
57
|
36
|
635
|
419
|
36
|
1183
|
|
Malignant hyperthermia, susceptibility to, 5
|
1
|
1
|
805
|
319
|
37
|
1163
|
|
Wilson disease
|
114
|
59
|
607
|
297
|
14
|
1091
|
|
Ehlers-Danlos syndrome, type 4
|
8
|
17
|
524
|
292
|
13
|
854
|
|
Hypercholesterolemia, familial, 1
|
90
|
72
|
380
|
227
|
5
|
774
|
|
BRCA2-related cancer predisposition
|
113
|
8
|
458
|
169
|
20
|
768
|
|
Breast-ovarian cancer, familial, susceptibility to, 1
|
80
|
7
|
378
|
261
|
25
|
751
|
|
Multiple endocrine neoplasia, type 2
|
12
|
7
|
449
|
219
|
4
|
691
|
|
Hypercholesterolemia, autosomal dominant, 3
|
2
|
1
|
412
|
198
|
20
|
633
|
|
Familial isolated arrhythmogenic right ventricular dysplasia
|
0 |
0 |
420
|
160
|
9
|
589
|
|
Familial adenomatous polyposis 2
|
54
|
31
|
299
|
130
|
7
|
521
|
|
Retinoblastoma
|
0 |
0 |
312
|
163
|
33
|
508
|
|
Hereditary pheochromocytoma and paraganglioma
|
34
|
21
|
315
|
102
|
2
|
474
|
|
Primary dilated cardiomyopathy
|
11
|
14
|
274
|
126
|
7
|
432
|
|
Peutz-Jeghers syndrome
|
1
|
0 |
215
|
193
|
3
|
412
|
|
BRCA1-related cancer predisposition
|
64
|
4
|
189
|
101
|
13
|
371
|
|
Arrhythmogenic right ventricular dysplasia 5
|
1
|
0 |
253
|
88
|
10
|
352
|
|
Juvenile polyposis syndrome
|
1
|
1
|
210
|
103
|
5
|
320
|
|
Loeys-Dietz syndrome 2
|
1
|
2
|
187
|
105
|
6
|
301
|
|
Multiple endocrine neoplasia, type 1
|
7
|
2
|
172
|
101
|
2
|
284
|
|
Wilms tumor 1
|
0 |
2
|
173
|
100
|
4
|
279
|
|
Neurofibromatosis, type 2
|
0 |
3
|
175
|
80
|
5
|
263
|
|
Li-Fraumeni syndrome
|
14
|
10
|
146
|
90
|
2
|
262
|
|
Aneurysm-osteoarthritis syndrome
|
2
|
6
|
117
|
101
|
6
|
232
|
|
Juvenile polyposis/hereditary hemorrhagic telangiectasia syndrome
|
2
|
0 |
113
|
108
|
0 |
223
|
|
Von Hippel-Lindau syndrome
|
2
|
2
|
138
|
67
|
0 |
209
|
|
Loeys-Dietz syndrome
|
1
|
1
|
128
|
73
|
3
|
206
|
|
PTEN hamartoma tumor syndrome
|
10
|
1
|
90
|
66
|
0 |
167
|
|
Fabry disease
|
11
|
5
|
72
|
20
|
0 |
108
|
|
Ornithine carbamoyltransferase deficiency
|
3
|
1
|
56
|
35
|
1
|
96
|
|
Brugada syndrome
|
24
|
24
|
4
|
0 |
0 |
52
|
|
Congenital long QT syndrome
|
4
|
4
|
4
|
0 |
0 |
12
|
|
Hypercholesterolemia, autosomal dominant, type B
|
2
|
0 |
1
|
0 |
0 |
3
|
The information on this website is not intended for direct
diagnostic use or medical decision-making without review by a
genetics professional. Individuals should not change their
health behavior solely on the basis of information contained on
this website. The submitted information has not been verified.
If you have questions about the information contained on this
website, please see a health care professional.