If a variant has more than one submission, it may be counted in more than one significance column. If this is the
case, the total number of variants will be less than the sum of the other cells.
| pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
total |
|
1530
|
959
|
2217
|
206
|
292
|
5204
|
Gene and significance breakdown #
Total genes and gene combinations: 23
| Gene or gene combination |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
total |
|
GLA, RPL36A-HNRNPH2
|
705
|
352
|
262
|
16
|
21
|
1356
|
|
ABCB11
|
146
|
69
|
367
|
33
|
41
|
656
|
|
CFH
|
105
|
75
|
377
|
24
|
46
|
627
|
|
ABCB4
|
117
|
62
|
334
|
38
|
21
|
572
|
|
ALPL
|
190
|
200
|
91
|
14
|
18
|
513
|
|
ATP8B1
|
66
|
30
|
130
|
32
|
38
|
296
|
|
CFI
|
44
|
86
|
128
|
9
|
23
|
290
|
|
C3
|
17
|
17
|
196
|
13
|
28
|
271
|
|
CD46
|
34
|
6
|
119
|
5
|
12
|
176
|
|
THBD
|
0 |
2
|
94
|
12
|
10
|
118
|
|
TK2
|
32
|
37
|
27
|
1
|
7
|
104
|
|
DGKE
|
32
|
7
|
25
|
1
|
6
|
71
|
|
CFB
|
6
|
5
|
29
|
3
|
16
|
59
|
|
ABCB11, LOC126806400
|
10
|
7
|
19
|
1
|
2
|
39
|
|
ENPP1
|
15
|
1
|
4
|
0 |
0 |
20
|
|
CD46, LOC129932405
|
1
|
1
|
8
|
2
|
1
|
13
|
|
ATP8B1, LOC126862761
|
1
|
1
|
5
|
1
|
0 |
8
|
|
ABCB4, LOC129998756
|
4
|
1
|
1
|
1
|
0 |
7
|
|
LOC130059156, TK2
|
3
|
0 |
0 |
0 |
1
|
4
|
|
ABCB4, LOC129998757
|
0 |
0 |
1
|
0 |
0 |
1
|
|
C2, CFB
|
0 |
0 |
0 |
0 |
1
|
1
|
|
CCN2, CTAGE9, ENPP1, ENPP3, LINC01013, LOC111365199, LOC123864069, LOC123864070, LOC126859789, LOC126859790, LOC129997167, LOC129997168, MIR548AJ1, MIR548H5, OR2A4
|
1
|
0 |
0 |
0 |
0 |
1
|
|
GLA, HNRNPH2, RPL36A-HNRNPH2
|
1
|
0 |
0 |
0 |
0 |
1
|
Condition and significance breakdown #
| Condition |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
total |
|
Fabry disease
|
706
|
352
|
262
|
16
|
21
|
1357
|
|
Familial intrahepatic cholestasis
|
304
|
141
|
696
|
76
|
81
|
1298
|
|
Atypical hemolytic-uremic syndrome
|
151
|
67
|
412
|
23
|
30
|
683
|
|
Hypophosphatasia
|
190
|
200
|
91
|
14
|
18
|
513
|
|
Basal laminar drusen; Factor H deficiency; Age related macular degeneration 4; Atypical hemolytic-uremic syndrome
|
0 |
21
|
137
|
12
|
46
|
216
|
|
CFI-related disorder
|
35
|
70
|
75
|
6
|
23
|
209
|
|
Low phospholipid associated cholelithiasis; Familial intrahepatic cholestasis
|
20
|
24
|
106
|
30
|
21
|
201
|
|
Thrombomodulin-related bleeding disorder
|
0 |
2
|
94
|
12
|
10
|
118
|
|
Atypical hemolytic-uremic syndrome; Complement component 3 deficiency; C3 glomerulonephritis
|
0 |
0 |
79
|
5
|
28
|
112
|
|
Mitochondrial disease
|
35
|
37
|
27
|
1
|
8
|
108
|
|
Age related macular degeneration 4
|
12
|
5
|
69
|
4
|
0 |
90
|
|
Low phospholipid associated cholelithiasis
|
20
|
5
|
55
|
0 |
0 |
80
|
|
C3 glomerulonephritis
|
0 |
1
|
49
|
1
|
0 |
51
|
|
Complement component 3 deficiency
|
17
|
5
|
4
|
0 |
0 |
26
|
|
Age related macular degeneration 4; Atypical hemolytic-uremic syndrome
|
2
|
7
|
14
|
1
|
0 |
24
|
|
Immunoglobulin-mediated membranoproliferative glomerulonephritis; Mesangiocapillary glomerulonephritis
|
0 |
0 |
9
|
1
|
6
|
16
|
|
Arterial calcification, generalized, of infancy, 1
|
10
|
1
|
4
|
0 |
0 |
15
|
|
Factor H deficiency
|
3
|
3
|
8
|
1
|
0 |
15
|
|
Atypical hemolytic-uremic syndrome; C3 glomerulonephritis
|
0 |
3
|
9
|
1
|
0 |
13
|
|
Factor H deficiency; Atypical hemolytic-uremic syndrome
|
3
|
4
|
2
|
0 |
0 |
9
|
|
Factor H deficiency; Age related macular degeneration 4; Atypical hemolytic-uremic syndrome
|
2
|
2
|
2
|
2
|
0 |
8
|
|
Arterial calcification, generalized, of infancy, 1; Hypophosphatemic rickets, autosomal recessive, 2
|
7
|
0 |
0 |
0 |
0 |
7
|
|
Atypical hemolytic-uremic syndrome; Mesangiocapillary glomerulonephritis
|
2
|
1
|
4
|
0 |
0 |
7
|
|
Factor I deficiency
|
0 |
5
|
2
|
0 |
0 |
7
|
|
Basal laminar drusen; Age related macular degeneration 4
|
3
|
0 |
2
|
0 |
0 |
5
|
|
Mesangiocapillary glomerulonephritis
|
4
|
0 |
1
|
0 |
0 |
5
|
|
Basal laminar drusen
|
1
|
1
|
1
|
0 |
0 |
3
|
|
Basal laminar drusen; Atypical hemolytic-uremic syndrome
|
2
|
0 |
1
|
0 |
0 |
3
|
|
Factor H deficiency; Age related macular degeneration 4
|
1
|
1
|
0 |
0 |
0 |
2
|
|
Basal laminar drusen; Age related macular degeneration 4; Atypical hemolytic-uremic syndrome
|
0 |
0 |
1
|
0 |
0 |
1
|
|
Basal laminar drusen; Factor H deficiency
|
0 |
0 |
1
|
0 |
0 |
1
|
|
Basal laminar drusen; Factor H deficiency; Age related macular degeneration 4
|
0 |
1
|
0 |
0 |
0 |
1
|
|
Basal laminar drusen; Factor H deficiency; Atypical hemolytic-uremic syndrome
|
1
|
0 |
0 |
0 |
0 |
1
|
|
Hypophosphatemic rickets, autosomal recessive, 2
|
1
|
0 |
0 |
0 |
0 |
1
|
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