If a variant has more than one submission, it may be counted in more than one significance column. If this is the
case, the total number of variants will be less than the sum of the other cells.
| pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
not provided |
total |
|
8
|
2
|
3
|
0 |
0 |
2688
|
2701
|
Gene and significance breakdown #
Total genes and gene combinations: 219
| Gene or gene combination |
pathogenic |
likely pathogenic |
uncertain significance |
not provided |
total |
|
KMT2D
|
0 |
0 |
0 |
90
|
90
|
|
BRCA2
|
0 |
0 |
0 |
86
|
86
|
|
KMT2C
|
0 |
0 |
0 |
82
|
82
|
|
NOTCH1
|
1
|
0 |
0 |
66
|
67
|
|
TSC2
|
0 |
0 |
0 |
55
|
55
|
|
RECQL4
|
0 |
0 |
0 |
54
|
54
|
|
APC
|
0 |
0 |
0 |
50
|
50
|
|
ATM
|
0 |
0 |
0 |
45
|
45
|
|
FANCA
|
0 |
0 |
0 |
45
|
45
|
|
SETD2
|
0 |
0 |
0 |
45
|
45
|
|
TET2
|
0 |
0 |
0 |
43
|
43
|
|
WRN
|
0 |
0 |
0 |
43
|
43
|
|
BIVM-ERCC5, ERCC5
|
0 |
0 |
0 |
40
|
40
|
|
BRCA1
|
0 |
0 |
0 |
38
|
38
|
|
ERCC2
|
0 |
0 |
0 |
38
|
38
|
|
EP300
|
1
|
0 |
0 |
33
|
34
|
|
TNFRSF14
|
0 |
0 |
0 |
33
|
33
|
|
ECT2L
|
0 |
0 |
0 |
32
|
32
|
|
ERBB2
|
0 |
0 |
0 |
32
|
32
|
|
PMS2
|
0 |
0 |
0 |
31
|
31
|
|
CIC
|
0 |
0 |
0 |
30
|
30
|
|
CREBBP
|
0 |
0 |
0 |
30
|
30
|
|
MET
|
0 |
0 |
0 |
30
|
30
|
|
NOTCH2
|
0 |
0 |
0 |
30
|
30
|
|
ALK
|
0 |
0 |
0 |
29
|
29
|
|
BLM
|
0 |
0 |
0 |
29
|
29
|
|
HNF1A
|
0 |
0 |
0 |
29
|
29
|
|
ERCC4
|
0 |
0 |
0 |
28
|
28
|
|
ASXL1
|
0 |
0 |
0 |
27
|
27
|
|
GNAS
|
0 |
0 |
0 |
27
|
27
|
|
XPC
|
0 |
0 |
0 |
27
|
27
|
|
BRIP1
|
0 |
0 |
0 |
26
|
26
|
|
JAK3
|
0 |
0 |
0 |
25
|
25
|
|
MPL
|
0 |
0 |
0 |
25
|
25
|
|
PDGFRA
|
0 |
0 |
0 |
25
|
25
|
|
TSC1
|
0 |
0 |
0 |
24
|
24
|
|
CARD11
|
0 |
0 |
0 |
23
|
23
|
|
KDR
|
0 |
0 |
0 |
23
|
23
|
|
RET
|
0 |
0 |
0 |
23
|
23
|
|
PALB2
|
0 |
0 |
0 |
22
|
22
|
|
PMS1
|
0 |
0 |
0 |
22
|
22
|
|
PTCH1
|
0 |
0 |
0 |
22
|
22
|
|
ATRX
|
0 |
0 |
0 |
21
|
21
|
|
FLT3
|
0 |
0 |
0 |
21
|
21
|
|
MUTYH
|
0 |
0 |
0 |
21
|
21
|
|
CDH1
|
0 |
0 |
0 |
20
|
20
|
|
IL7R
|
0 |
0 |
0 |
20
|
20
|
|
MSH6
|
0 |
0 |
0 |
20
|
20
|
|
ABL1
|
0 |
0 |
0 |
19
|
19
|
|
AMER1
|
0 |
0 |
0 |
19
|
19
|
|
BUB1B
|
0 |
0 |
0 |
19
|
19
|
|
EGFR
|
0 |
0 |
0 |
19
|
19
|
|
FGFR3
|
0 |
0 |
0 |
19
|
19
|
|
FLCN
|
0 |
0 |
0 |
19
|
19
|
|
MSH2
|
0 |
0 |
0 |
19
|
19
|
|
ARID2
|
0 |
0 |
0 |
18
|
18
|
|
ATM, C11orf65
|
0 |
0 |
0 |
17
|
17
|
|
CDK12
|
0 |
0 |
0 |
17
|
17
|
|
EXT2
|
0 |
0 |
0 |
17
|
17
|
|
MLH1
|
0 |
0 |
0 |
17
|
17
|
|
PRDM1
|
0 |
0 |
0 |
17
|
17
|
|
SMARCA4
|
0 |
0 |
0 |
17
|
17
|
|
TNFAIP3
|
0 |
0 |
0 |
17
|
17
|
|
DICER1
|
0 |
0 |
0 |
16
|
16
|
|
NF1
|
0 |
0 |
0 |
16
|
16
|
|
FANCA, ZNF276
|
0 |
0 |
0 |
15
|
15
|
|
FANCG
|
0 |
0 |
0 |
15
|
15
|
|
INSL6, JAK2
|
0 |
0 |
0 |
15
|
15
|
|
NBN
|
0 |
0 |
0 |
15
|
15
|
|
SMO
|
0 |
0 |
0 |
15
|
15
|
|
TP53
|
0 |
0 |
0 |
14
|
14
|
|
BCOR
|
0 |
0 |
0 |
13
|
13
|
|
CBLB
|
0 |
0 |
0 |
13
|
13
|
|
ERCC3
|
0 |
0 |
0 |
13
|
13
|
|
FANCD2, LOC107303338
|
0 |
0 |
0 |
13
|
13
|
|
FANCE
|
0 |
0 |
0 |
13
|
13
|
|
RB1
|
0 |
0 |
0 |
13
|
13
|
|
TSHR
|
0 |
0 |
0 |
13
|
13
|
|
AOPEP, FANCC
|
0 |
0 |
0 |
12
|
12
|
|
CBL
|
0 |
0 |
0 |
12
|
12
|
|
CDKN2A
|
0 |
0 |
0 |
12
|
12
|
|
KIT
|
0 |
0 |
0 |
12
|
12
|
|
NFE2L2
|
0 |
0 |
0 |
12
|
12
|
|
ARID1A
|
0 |
0 |
0 |
10
|
10
|
|
CHEK2
|
0 |
0 |
0 |
10
|
10
|
|
EZH2
|
0 |
0 |
0 |
10
|
10
|
|
FGFR2
|
0 |
0 |
0 |
10
|
10
|
|
SMARCB1
|
0 |
0 |
0 |
9
|
9
|
|
BCL6, LOC100131635
|
0 |
0 |
0 |
8
|
8
|
|
BRCA1, LOC126862571
|
0 |
0 |
0 |
8
|
8
|
|
FANCF
|
0 |
0 |
0 |
8
|
8
|
|
FH
|
0 |
0 |
0 |
8
|
8
|
|
IDH1
|
0 |
0 |
0 |
8
|
8
|
|
KDM6A
|
0 |
0 |
0 |
8
|
8
|
|
PAX5
|
0 |
0 |
0 |
8
|
8
|
|
PBRM1
|
0 |
0 |
0 |
8
|
8
|
|
SUFU
|
0 |
0 |
0 |
8
|
8
|
|
TENT5C
|
0 |
0 |
0 |
8
|
8
|
|
WAS
|
0 |
0 |
0 |
8
|
8
|
|
ARHGAP26
|
0 |
0 |
0 |
7
|
7
|
|
BAP1
|
0 |
0 |
0 |
7
|
7
|
|
BCOR, LOC126863239
|
0 |
0 |
0 |
7
|
7
|
|
CD79A
|
0 |
0 |
0 |
7
|
7
|
|
CYLD
|
0 |
0 |
0 |
7
|
7
|
|
FBXW7
|
0 |
0 |
0 |
7
|
7
|
|
JAK1
|
0 |
0 |
0 |
7
|
7
|
|
KDM5C
|
0 |
0 |
0 |
7
|
7
|
|
NF2
|
0 |
0 |
0 |
7
|
7
|
|
XPA
|
0 |
0 |
0 |
7
|
7
|
|
EXT1
|
0 |
0 |
0 |
6
|
6
|
|
FUBP1
|
0 |
0 |
0 |
6
|
6
|
|
KLF6
|
0 |
0 |
0 |
6
|
6
|
|
BMPR1A
|
0 |
0 |
0 |
5
|
5
|
|
CRLF2
|
0 |
0 |
0 |
5
|
5
|
|
DNM2
|
0 |
0 |
0 |
5
|
5
|
|
DNMT3A
|
0 |
0 |
0 |
5
|
5
|
|
FANCC
|
0 |
0 |
0 |
5
|
5
|
|
FANCD2, FANCD2OS
|
0 |
0 |
0 |
5
|
5
|
|
FAS
|
0 |
0 |
0 |
5
|
5
|
|
GATA2
|
0 |
0 |
0 |
5
|
5
|
|
LOC100507346, PTCH1
|
0 |
0 |
0 |
5
|
5
|
|
MED12
|
0 |
0 |
0 |
5
|
5
|
|
PPP2R1A
|
0 |
0 |
0 |
5
|
5
|
|
PTPN11
|
0 |
0 |
0 |
5
|
5
|
|
SDHD
|
0 |
0 |
0 |
5
|
5
|
|
WT1
|
0 |
0 |
0 |
5
|
5
|
|
BRAF
|
0 |
0 |
0 |
4
|
4
|
|
DDB2
|
0 |
0 |
0 |
4
|
4
|
|
FBXO11
|
0 |
0 |
0 |
4
|
4
|
|
GPC3
|
0 |
0 |
0 |
4
|
4
|
|
MEN1
|
0 |
0 |
0 |
4
|
4
|
|
MYD88
|
0 |
0 |
0 |
4
|
4
|
|
NPM1
|
0 |
0 |
0 |
4
|
4
|
|
SDHB
|
0 |
0 |
0 |
4
|
4
|
|
SMAD4
|
0 |
0 |
0 |
4
|
4
|
|
ZRSR2
|
0 |
0 |
0 |
4
|
4
|
|
AKT1
|
0 |
0 |
0 |
3
|
3
|
|
BIVM-ERCC5, ERCC5, LOC126861834
|
0 |
0 |
0 |
3
|
3
|
|
CBLB, LOC126806757
|
0 |
0 |
0 |
3
|
3
|
|
CD79B, GH-LCR
|
0 |
0 |
0 |
3
|
3
|
|
CDC73
|
0 |
0 |
0 |
3
|
3
|
|
CDK4
|
0 |
0 |
0 |
3
|
3
|
|
CEP128, TSHR
|
0 |
0 |
0 |
3
|
3
|
|
ERCC4, LOC130058543
|
0 |
0 |
0 |
3
|
3
|
|
FANCE, LOC129996245
|
0 |
0 |
0 |
3
|
3
|
|
FANCF, LOC130005443
|
0 |
0 |
0 |
3
|
3
|
|
FIP1L1
|
0 |
0 |
0 |
3
|
3
|
|
GATA3
|
0 |
0 |
0 |
3
|
3
|
|
KCNK12, MSH2
|
0 |
0 |
0 |
3
|
3
|
|
KMT2D, LOC126861520
|
0 |
0 |
0 |
3
|
3
|
|
KRAS
|
0 |
0 |
0 |
3
|
3
|
|
LOC129936244, XPC
|
0 |
0 |
0 |
3
|
3
|
|
LOC130062899, STK11
|
0 |
0 |
0 |
3
|
3
|
|
PHOX2B
|
0 |
0 |
0 |
3
|
3
|
|
PIK3CA
|
0 |
0 |
0 |
3
|
3
|
|
SDHC
|
0 |
0 |
0 |
3
|
3
|
|
SOCS1
|
0 |
0 |
0 |
3
|
3
|
|
VHL
|
0 |
0 |
0 |
3
|
3
|
|
C12orf43, HNF1A
|
0 |
0 |
0 |
2
|
2
|
|
C9
|
0 |
2
|
0 |
0 |
2
|
|
CDK4, TSPAN31
|
0 |
0 |
0 |
2
|
2
|
|
CTNNB1, LOC126806658
|
0 |
0 |
0 |
2
|
2
|
|
FANCA, LOC112486223
|
0 |
0 |
0 |
2
|
2
|
|
FANCD2
|
0 |
0 |
0 |
2
|
2
|
|
FBXO11, MSH6
|
0 |
0 |
0 |
2
|
2
|
|
GATA1
|
0 |
0 |
0 |
2
|
2
|
|
KMT2C, LOC129999675
|
0 |
0 |
0 |
2
|
2
|
|
LOC107303340, VHL
|
0 |
0 |
0 |
2
|
2
|
|
LOC126859807, TNFAIP3
|
0 |
0 |
0 |
2
|
2
|
|
LOC130002133, PTCH1
|
0 |
0 |
0 |
2
|
2
|
|
PHF6
|
0 |
0 |
0 |
2
|
2
|
|
PIK3R1
|
0 |
0 |
0 |
2
|
2
|
|
XPO1
|
0 |
0 |
0 |
2
|
2
|
|
intergenic
|
0 |
0 |
0 |
1
|
1
|
|
ABL1, LOC107980440
|
0 |
0 |
0 |
1
|
1
|
|
ARID1A, LOC126805670
|
0 |
0 |
0 |
1
|
1
|
|
BCL6
|
0 |
0 |
0 |
1
|
1
|
|
BUB1B, BUB1B-PAK6
|
0 |
0 |
0 |
1
|
1
|
|
BUB1B, LOC130056830
|
0 |
0 |
0 |
1
|
1
|
|
CDKL5
|
1
|
0 |
0 |
0 |
1
|
|
CDKN1C
|
1
|
0 |
0 |
0 |
1
|
|
CEBPA
|
0 |
0 |
0 |
1
|
1
|
|
CIC, LOC130064572
|
0 |
0 |
0 |
1
|
1
|
|
CTNNB1
|
0 |
0 |
0 |
1
|
1
|
|
CTNNB1, LOC126806659
|
0 |
0 |
0 |
1
|
1
|
|
ECT2L, LOC129997295
|
0 |
0 |
0 |
1
|
1
|
|
EGFR, LOC126860048
|
0 |
0 |
0 |
1
|
1
|
|
EP300, LOC126863158
|
0 |
0 |
0 |
1
|
1
|
|
EPCAM
|
1
|
0 |
0 |
0 |
1
|
|
FANCA, LOC130059837
|
0 |
0 |
0 |
1
|
1
|
|
FOXL2
|
0 |
0 |
0 |
1
|
1
|
|
FUBP1, LOC129930801
|
0 |
0 |
0 |
1
|
1
|
|
GLRA1
|
1
|
0 |
0 |
0 |
1
|
|
GNA11
|
0 |
0 |
0 |
1
|
1
|
|
GSK3A, LOC130064563
|
0 |
0 |
1
|
0 |
1
|
|
HRAS, LRRC56
|
0 |
0 |
0 |
1
|
1
|
|
HSD17B4
|
1
|
0 |
0 |
0 |
1
|
|
JAK1, LOC126805749
|
0 |
0 |
0 |
1
|
1
|
|
JAK1, LOC129930680
|
0 |
0 |
0 |
1
|
1
|
|
LOC105376032, PAX5
|
0 |
0 |
0 |
1
|
1
|
|
LOC126807054, PDGFRA
|
0 |
0 |
0 |
1
|
1
|
|
LOC126859755, PRDM1
|
0 |
0 |
0 |
1
|
1
|
|
LOC126860342, WRN
|
0 |
0 |
0 |
1
|
1
|
|
LOC126861339, SDHD
|
0 |
0 |
0 |
1
|
1
|
|
LOC126863275, MED12
|
0 |
0 |
0 |
1
|
1
|
|
LOC129999303, SMO
|
0 |
0 |
0 |
1
|
1
|
|
LOC130001411, RECQL4
|
0 |
0 |
0 |
1
|
1
|
|
LOC130058210, TSC2
|
0 |
0 |
0 |
1
|
1
|
|
LOC130058479, SOCS1
|
0 |
0 |
0 |
1
|
1
|
|
NEDD4L
|
0 |
0 |
1
|
0 |
1
|
|
NRAS
|
0 |
0 |
0 |
1
|
1
|
|
PKD1, TSC2
|
0 |
0 |
0 |
1
|
1
|
|
PLG
|
1
|
0 |
0 |
0 |
1
|
|
PRKAR1A
|
0 |
0 |
0 |
1
|
1
|
|
PTEN
|
0 |
0 |
0 |
1
|
1
|
|
RMI2, SOCS1
|
0 |
0 |
0 |
1
|
1
|
|
SCN5A
|
0 |
0 |
1
|
0 |
1
|
|
SF3B1
|
0 |
0 |
0 |
1
|
1
|
|
STK11
|
0 |
0 |
0 |
1
|
1
|
Condition and significance breakdown #
The information on this website is not intended for direct
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