If a variant has more than one submission, it may be counted in more than one significance column. If this is the
case, the total number of variants will be less than the sum of the other cells.
| pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
not provided |
total |
|
218
|
67
|
315
|
136
|
128
|
3
|
808
|
Gene and significance breakdown #
Total genes and gene combinations: 86
| Gene or gene combination |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
not provided |
total |
|
CRX
|
105
|
24
|
218
|
119
|
72
|
2
|
483
|
|
PRPH2
|
5
|
2
|
37
|
8
|
35
|
0 |
87
|
|
UNC119
|
0 |
0 |
12
|
4
|
14
|
0 |
30
|
|
ABCA4
|
17
|
5
|
4
|
0 |
0 |
1
|
27
|
|
PROM1
|
14
|
2
|
2
|
0 |
0 |
0 |
17
|
|
USH2A
|
4
|
1
|
4
|
0 |
0 |
0 |
9
|
|
CACNA1F
|
5
|
1
|
1
|
0 |
0 |
0 |
7
|
|
CRB1
|
2
|
3
|
2
|
0 |
0 |
0 |
7
|
|
LOC130060555, UNC119
|
0 |
0 |
5
|
1
|
1
|
0 |
7
|
|
GUCY2D
|
1
|
3
|
1
|
0 |
0 |
0 |
5
|
|
TTLL5
|
4
|
1
|
0 |
0 |
0 |
0 |
5
|
|
ABCA4, LOC126805793
|
2
|
2
|
0 |
0 |
0 |
0 |
4
|
|
ADAM9
|
4
|
0 |
0 |
0 |
0 |
0 |
4
|
|
CDHR1
|
2
|
2
|
0 |
0 |
0 |
0 |
4
|
|
CEP78
|
4
|
0 |
0 |
0 |
0 |
0 |
4
|
|
CERKL
|
3
|
1
|
0 |
0 |
0 |
0 |
4
|
|
CNGA3
|
1
|
3
|
0 |
0 |
0 |
0 |
4
|
|
GPHN, RDH12
|
3
|
1
|
0 |
0 |
0 |
0 |
4
|
|
NMNAT1
|
2
|
2
|
0 |
0 |
0 |
0 |
4
|
|
ABCA4, LOC126805794
|
2
|
1
|
0 |
0 |
0 |
0 |
3
|
|
CABP4
|
1
|
2
|
0 |
0 |
0 |
0 |
3
|
|
EYS
|
1
|
0 |
2
|
0 |
0 |
0 |
3
|
|
RPGRIP1
|
3
|
0 |
0 |
0 |
0 |
0 |
3
|
|
ACBD5
|
0 |
0 |
2
|
0 |
0 |
0 |
2
|
|
C10orf105, CDH23
|
0 |
0 |
1
|
1
|
0 |
0 |
2
|
|
CDH23
|
0 |
0 |
1
|
1
|
0 |
0 |
2
|
|
CFAP410
|
0 |
1
|
1
|
0 |
0 |
0 |
2
|
|
CLN3
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
|
ERCC6
|
0 |
0 |
0 |
0 |
2
|
0 |
2
|
|
GUCA1A, GUCA1ANB-GUCA1A
|
1
|
1
|
0 |
0 |
0 |
0 |
2
|
|
KCNV2
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
|
MERTK
|
0 |
0 |
2
|
0 |
0 |
0 |
2
|
|
MFSD8
|
0 |
1
|
1
|
0 |
0 |
0 |
2
|
|
MYO7A
|
0 |
0 |
2
|
0 |
0 |
0 |
2
|
|
NR2E3
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
|
PCARE
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
|
RAB28
|
1
|
1
|
0 |
0 |
0 |
0 |
2
|
|
RPGR
|
1
|
1
|
0 |
0 |
0 |
0 |
2
|
|
SETX
|
0 |
0 |
0 |
2
|
0 |
0 |
2
|
|
SGSH
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
|
ADAM9, LOC130000261
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
AIPL1
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
ALMS1
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
ARL6
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
BICRA, C5AR1, C5AR2, CCDC9, CRX, DHX34, EHD2, INAFM1, KPTN, LINC01595, LOC112552166, LOC116286191, LOC121627882, LOC121627883, LOC121852990, LOC125371537, LOC125371538, LOC125371539, LOC125371540, LOC130064806, LOC130064807, LOC130064808, LOC130064809, LOC130064810, LOC130064811, LOC130064812, LOC130064813, LOC130064814, LOC130064815, LOC130064816, LOC130064817, LOC130064818, LOC130064819, LOC130064820, LOC130064821, LOC130064822, LOC130064823, LOC130064824, LOC130064825, LOC130064826, LOC130064827, LOC130064828, LOC130064829, LOC130064830, LOC130064831, MEIS3, NAPA, NOP53, SELENOW, SLC8A2, SNORD23, SULT2A1, TPRX1, TPRX2, ZNF541
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
CACNA2D4
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
CEP290
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
CERKL, ITGA4
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
CERKL, LOC129935214
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
CFAP410, LOC130066823
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
CNGA1, LOC101927157
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
CNGB3
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
CREBBP
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
CRX, LINC01595, SULT2A1, TPRX1, TPRX2
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
CRX, SULT2A1
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
CRX, SULT2A1, TPRX1
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
CRX, TPRX2
|
0 |
0 |
1
|
0 |
1
|
0 |
1
|
|
CUX2
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
DRAM2
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
EYS, LOC132089419, LOC132089420, LOC132089421, LOC132089422, LOC132089423, LOC132089424, LOC132089425, LOC132089426, LOC132089427, LOC132089428, LOC132089429, LOC132090758, LOC132090759, LOC132205963, LOC132205964
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
FAM161A
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
GUCA1A, GUCA1ANB-GUCA1A, GUCA1B
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
IFT81
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
IMPG1
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
IMPG2
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
LOC125384566, LOC130065345, LOC130065346, LOC130065347, MIR103A2, MIR103B2, PANK2
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
LOC130068202, RP2
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
MECP2
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
NLGN3
|
0 |
0 |
0 |
0 |
1
|
0 |
1
|
|
OCA2
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
OPA1
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
PANK2
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
PDE6B
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
POC1B, POC1B-DUSP6
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
PRPF31
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
RAD21
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
RBP3
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
RHO
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
RP1
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
RP1L1
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
RPE65
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
SCLT1
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
SEMA4A
|
0 |
0 |
0 |
0 |
1
|
0 |
1
|
|
SNRNP200
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
SSBP1
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
TRPM1
|
0 |
0 |
0 |
0 |
1
|
0 |
1
|
Submitter and significance breakdown #
| Submitter |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
not provided |
total |
|
Labcorp Genetics (formerly Invitae), Labcorp
|
85
|
10
|
142
|
93
|
14
|
0 |
344
|
|
Illumina Laboratory Services, Illumina
|
0 |
0 |
127
|
41
|
113
|
0 |
242
|
|
Sharon lab, Hadassah-Hebrew University Medical Center
|
26
|
9
|
0 |
0 |
0 |
0 |
35
|
|
Cambridge Genomics Laboratory, East Genomic Laboratory Hub, NHS Genomic Medicine Service
|
5
|
3
|
17
|
4
|
5
|
0 |
34
|
|
Molecular Genetics Laboratory, Institute for Ophthalmic Research
|
30
|
0 |
1
|
0 |
0 |
0 |
31
|
|
Ophthalmic Genetics Group, Institute of Molecular and Clinical Ophthalmology Basel
|
19
|
8
|
4
|
0 |
0 |
0 |
31
|
|
Lab De Baere, Eye and Developmental Genetics Lab, Ghent University
|
13
|
9
|
6
|
0 |
0 |
0 |
28
|
|
Department of Clinical Genetics, Copenhagen University Hospital, Rigshospitalet
|
7
|
11
|
1
|
0 |
0 |
0 |
19
|
|
Laboratory of Genetics in Ophthalmology, Institut Imagine
|
15
|
0 |
0 |
0 |
0 |
0 |
15
|
|
Joint Genome Diagnostic Labs from Nijmegen and Maastricht, Radboudumc and MUMC+
|
6
|
0 |
5
|
0 |
0 |
0 |
11
|
|
3billion
|
3
|
6
|
1
|
0 |
0 |
0 |
10
|
|
OMIM
|
10
|
0 |
0 |
0 |
0 |
0 |
10
|
|
NEI Ophthalmic Genomics Laboratory, National Institutes of Health
|
4
|
1
|
4
|
0 |
0 |
0 |
9
|
|
DBGen Ocular Genomics
|
2
|
1
|
3
|
0 |
0 |
0 |
6
|
|
Broad Center for Mendelian Genomics, Broad Institute of MIT and Harvard
|
0 |
0 |
3
|
0 |
0 |
0 |
3
|
|
Department of Pathology and Laboratory Medicine, Sinai Health System
|
0 |
0 |
3
|
0 |
0 |
0 |
3
|
|
Mendelics
|
2
|
1
|
0 |
0 |
0 |
0 |
3
|
|
Bioscientia Institut fuer Medizinische Diagnostik GmbH, Sonic Healthcare
|
0 |
2
|
0 |
0 |
0 |
0 |
2
|
|
Fulgent Genetics, Fulgent Genetics
|
0 |
0 |
0 |
1
|
1
|
0 |
2
|
|
Genomic Medicine Center of Excellence, King Faisal Specialist Hospital and Research Centre
|
0 |
0 |
1
|
1
|
0 |
0 |
2
|
|
Genomics England Pilot Project, Genomics England
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
|
Institute of Medical Genetics and Applied Genomics, University Hospital Tübingen
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
|
Research Institute for Ophthalmology and Vision Science, Shahid Beheshti University of Medical Sciences
|
2
|
0 |
0 |
0 |
0 |
0 |
2
|
|
SingHealth Duke-NUS Institute of Precision Medicine
|
1
|
1
|
0 |
0 |
0 |
0 |
2
|
|
Department of Genetics, Fundacion Jimenez Diaz University Hospital
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
Department of Medical Genetics, Erciyes University Faculty of Medicine
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
Department of Molecular and Human Genetics, Baylor College of Medicine
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
Department of Ophthalmology and Visual Sciences Kyoto University
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
Eye Genetics Research Group, Children's Medical Research Institute
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
GeneReviews
|
0 |
0 |
0 |
0 |
0 |
1
|
1
|
|
Genetics and Molecular Pathology, SA Pathology
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
Genome-Nilou Lab
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
GenomeConnect - Invitae Patient Insights Network
|
0 |
0 |
0 |
0 |
0 |
1
|
1
|
|
GenomeConnect, ClinGen
|
0 |
0 |
0 |
0 |
0 |
1
|
1
|
|
Genomic Research Center, Shahid Beheshti University of Medical Sciences
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
Institute of Human Genetics, University of Goettingen
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
Institute of Human Genetics, University of Leipzig Medical Center
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
Institute of Medical Molecular Genetics, University of Zurich
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
Laboratory for Molecular Medicine, Mass General Brigham Personalized Medicine
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
MGZ Medical Genetics Center
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
Medical Genetics Laboratory, Niloo Shiraz Laboratory
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
Molecular Diagnostics Laboratory, M Health Fairview: University of Minnesota
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
Ophthalmo-Genetics Lab, Instituto de Oftalmologia Conde de Valenciana
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
Pediatric/Medical Genetics, Ministry of Health, Qatif Central Hospital
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
UCLA Clinical Genomics Center, UCLA
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
The information on this website is not intended for direct
diagnostic use or medical decision-making without review by a
genetics professional. Individuals should not change their
health behavior solely on the basis of information contained on
this website. The submitted information has not been verified.
If you have questions about the information contained on this
website, please see a health care professional.