If a variant has more than one submission, it may be counted in more than one significance column. If this is the
case, the total number of variants will be less than the sum of the other cells.
| pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
not provided |
total |
|
129
|
74
|
1070
|
1366
|
126
|
4
|
2630
|
Gene and significance breakdown #
Total genes and gene combinations: 16
| Gene or gene combination |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
not provided |
total |
|
CIITA
|
61
|
41
|
634
|
995
|
81
|
2
|
1713
|
|
RFX5
|
30
|
13
|
215
|
133
|
20
|
1
|
402
|
|
RFXANK
|
19
|
12
|
93
|
148
|
8
|
0 |
262
|
|
RFXAP
|
9
|
2
|
63
|
33
|
10
|
0 |
114
|
|
LOC130009573, RFXAP
|
2
|
2
|
25
|
18
|
1
|
1
|
45
|
|
CIITA, LOC130058443
|
1
|
2
|
8
|
14
|
0 |
0 |
25
|
|
LOC130009575, RFXAP
|
2
|
1
|
9
|
11
|
0 |
0 |
23
|
|
NR2C2AP, RFXANK
|
1
|
1
|
8
|
10
|
3
|
0 |
21
|
|
LOC130009574, RFXAP
|
1
|
0 |
7
|
3
|
2
|
0 |
12
|
|
CIITA, LOC130058442
|
0 |
0 |
3
|
0 |
1
|
0 |
4
|
|
LOC126805858, RFX5
|
0 |
0 |
3
|
1
|
0 |
0 |
4
|
|
ABAT, ATF7IP2, CARHSP1, CIITA, CLEC16A, DEXI, EMP2, GRIN2A, HAPSTR1, LITAF, NUBP1, PMM2, PRM1, PRM2, PRM3, RMI2, SOCS1, TEKT5, TMEM186, TNP2, TVP23A, USP7
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
ADAM15, ADAMTSL4, ADAR, ANP32E, ANXA9, APH1A, AQP10, ARHGEF2, ARNT, ASH1L, ATP8B2, BCAN, BGLAP, BNIPL, C1orf54, C1orf56, C2CD4D, CA14, CCT3, CDC42SE1, CELF3, CERS2, CFAP141, CGN, CHRNB2, CHTOP, CIART, CKS1B, CLK2, CRABP2, CRCT1, CREB3L4, CRNN, CRTC2, CTSK, CTSS, DAP3, DCST1, DCST2, DENND4B, DPM3, ECM1, EFNA1, EFNA3, EFNA4, ENSA, ENTREP3, FALEC, FDPS, FLAD1, FLG, FLG2, GABPB2, GATAD2B, GBA1, GLMP, GOLPH3L, GON4L, GPATCH4, HAPLN2, HAX1, HCN3, HDGF, HORMAD1, HRNR, IL6R, ILF2, INSRR, INTS3, IQGAP3, ISG20L2, IVL, JTB, KCNN3, KHDC4, KPLCE, KPRP, KRTCAP2, LAMTOR2, LCE1A, LCE1B, LCE1C, LCE1D, LCE1E, LCE1F, LCE2A, LCE2B, LCE2C, LCE2D, LCE3A, LCE3B, LCE3C, LCE3D, LCE3E, LCE4A, LCE5A, LCE6A, LELP1, LENEP, LINGO4, LMNA, LOC101928034, LORICRIN, LTAP1, LYSMD1, MCL1, MEF2D, METTL25B, MEX3A, MINDY1, MIR9-1, MIR9-1HG, MLLT11, MRPL24, MRPL9, MRPS21, MSTO1, MTMR11, MTX1, MUC1, NAXE, NES, NPR1, NTRK1, NUP210L, OAZ3, OTUD7B, PAQR6, PBXIP1, PGLYRP3, PGLYRP4, PI4KB, PIP5K1A, PKLR, PLEKHO1, PMF1, PMF1-BGLAP, PMVK, POGZ, PRCC, PRPF3, PRR9, PRUNE1, PSMB4, PSMD4, PYGO2, RAB13, RAB25, RFX5, RHBG, RIIAD1, RIT1, RORC, RPRD2, RPS27, RPTN, RUSC1, RXFP4, S100A1, S100A10, S100A11, S100A12, S100A13, S100A14, S100A16, S100A2, S100A3, S100A4, S100A5, S100A6, S100A7, S100A7A, S100A8, S100A9, SCAMP3, SCNM1, SELENBP1, SEMA4A, SEMA6C, SETDB1, SF3B4, SH2D2A, SHC1, SHE, SLC25A44, SLC27A3, SLC39A1, SLC50A1, SMCP, SMG5, SNAPIN, SNX27, SPRR1A, SPRR1B, SPRR2A, SPRR2B, SPRR2D, SPRR2E, SPRR2F, SPRR2G, SPRR3, SPRR4, SSR2, SYT11, TARS2, TCHH, TCHHL1, TDRD10, TDRKH, THBS3, THEM4, THEM5, TMEM79, TMOD4, TNFAIP8L2, TPM3, TRIM46, TSACC, TTC24, TUFT1, UBAP2L, UBE2Q1, UBQLN4, VHLL, VPS45, VPS72, YY1AP1, ZBTB7B, ZNF687
|
0 |
0 |
1
|
0 |
0 |
0 |
1
|
|
ALG5, EXOSC8, RFXAP, SMAD9
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
CIITA, CLEC16A, DEXI, LITAF, PRM1, PRM2, PRM3, RMI2, SOCS1, TNP2
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
CIITA, EMP2, NUBP1, TEKT5, TVP23A
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
Submitter and significance breakdown #
| Submitter |
pathogenic |
likely pathogenic |
uncertain significance |
likely benign |
benign |
not provided |
total |
|
Labcorp Genetics (formerly Invitae), Labcorp
|
120
|
29
|
782
|
1329
|
93
|
0 |
2353
|
|
Natera, Inc.
|
2
|
27
|
248
|
55
|
30
|
0 |
362
|
|
Illumina Laboratory Services, Illumina
|
0 |
0 |
187
|
18
|
53
|
0 |
258
|
|
Genome-Nilou Lab
|
0 |
0 |
22
|
2
|
31
|
0 |
55
|
|
Women's Health and Genetics/Laboratory Corporation of America, LabCorp
|
5
|
7
|
0 |
0 |
0 |
0 |
12
|
|
Baylor Genetics
|
2
|
2
|
7
|
0 |
0 |
0 |
11
|
|
Center for Genomics, Ann and Robert H. Lurie Children's Hospital of Chicago
|
1
|
0 |
6
|
0 |
0 |
0 |
7
|
|
Biochemical Molecular Genetic Laboratory, King Abdulaziz Medical City
|
2
|
1
|
3
|
0 |
0 |
0 |
6
|
|
Genomic Medicine Center of Excellence, King Faisal Specialist Hospital and Research Centre
|
4
|
1
|
1
|
0 |
0 |
0 |
6
|
|
Fulgent Genetics, Fulgent Genetics
|
0 |
0 |
2
|
2
|
0 |
0 |
4
|
|
GenomeConnect - Invitae Patient Insights Network
|
0 |
0 |
0 |
0 |
0 |
4
|
4
|
|
New York Genome Center
|
0 |
0 |
3
|
0 |
0 |
0 |
3
|
|
Pathology and Clinical Laboratory Medicine, King Fahad Medical City
|
2
|
1
|
0 |
0 |
0 |
0 |
3
|
|
3billion
|
1
|
0 |
1
|
0 |
0 |
0 |
2
|
|
Institute of Human Genetics, University of Leipzig Medical Center
|
0 |
2
|
0 |
0 |
0 |
0 |
2
|
|
Laboratory for Molecular Medicine, Mass General Brigham Personalized Medicine
|
1
|
1
|
0 |
0 |
0 |
0 |
2
|
|
Clinic of Clinical Immunology with Stem Cell Bank, Expert Centre for Rare Diseases - PID, University Hospital "Alexandrovska"
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
Clinical Genetics DNA and cytogenetics Diagnostics Lab, Erasmus MC, Erasmus Medical Center
|
0 |
0 |
0 |
0 |
1
|
0 |
1
|
|
Department of Pathology and Laboratory Medicine, Sinai Health System
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
Diagnostic Laboratory, Department of Genetics, University Medical Center Groningen
|
0 |
0 |
0 |
1
|
0 |
0 |
1
|
|
Foundation for Research in Genetics and Endocrinology, FRIGE's Institute of Human Genetics
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
HudsonAlpha Institute for Biotechnology, HudsonAlpha Institute for Biotechnology
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
Intergen Genetics and Rare Diseases Diagnosis Center
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
Laboratorio de Genetica e Diagnostico Molecular, Hospital Israelita Albert Einstein
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
|
Quest Diagnostics Nichols Institute San Juan Capistrano
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
Randwick Genomics Laboratory, Prince of Wales Hospital Sydney, Australia, New South Wales Health Pathology
|
1
|
0 |
0 |
0 |
0 |
0 |
1
|
|
School of Computer Science, University of Waterloo
|
0 |
1
|
0 |
0 |
0 |
0 |
1
|
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