Total submissions: 2
| Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
|---|---|---|---|---|---|---|---|---|
| Ambry Genetics | RCV006657006 | SCV007555492 | uncertain significance | Cardiovascular phenotype | 2026-03-03 | criteria provided, single submitter | clinical testing | The p.E195D variant (also known as c.585A>C), located in coding exon 5 of the PTPN11 gene, results from an A to C substitution at nucleotide position 585. The glutamic acid at codon 195 is replaced by aspartic acid, an amino acid with highly similar properties. This amino acid position is conserved. In addition, the in silico prediction for this alteration is inconclusive. Based on the available evidence, the clinical significance of this variant remains unclear. |
| Fulgent Genetics, |
RCV005006808 | SCV005632284 | uncertain significance | Noonan syndrome 1; Juvenile myelomonocytic leukemia; Metachondromatosis; LEOPARD syndrome 1 | 2024-01-20 | criteria provided, single submitter | clinical testing |