Total submissions: 2
| Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
|---|---|---|---|---|---|---|---|---|
| Fulgent Genetics, |
RCV005036589 | SCV005664355 | uncertain significance | Sucrase-isomaltase deficiency | 2024-04-25 | criteria provided, single submitter | clinical testing | |
| Ambry Genetics | RCV002907099 | SCV003665965 | uncertain significance | Inborn genetic diseases | 2022-12-02 | criteria provided, single submitter | clinical testing | The c.2798A>G (p.Q933R) alteration is located in exon 25 (coding exon 24) of the SI gene. This alteration results from a A to G substitution at nucleotide position 2798, causing the glutamine (Q) at amino acid position 933 to be replaced by an arginine (R). Based on insufficient or conflicting evidence, the clinical significance of this alteration remains unclear. |